Pulmonary Atresia With Intact Septum Survival, Reintervention, and Days in Hospital Through Childhood: Contemporary Outcomes From a National Registry

Authors' conclusion

In a contemporary pulmonary atresia with intact ventricular septum cohort, transcatheter right ventricular decompression was the predominant initial intervention. This approach had lower in-hospital mortality compared with older multicenter series, with BiV repair achieved in more than half of the patients. Early mortality after nonantegrade flow augmentation remains high, likely due to nonmodifiable risk factors in severe cases. Long-term survival and hospital stay remain better for those amenable to BiV circulation, reflecting more favorable anatomy compared with those on the single-ventricle pathway, although reintervention is lower in the latter.