Heart failure & cardiomyopathies
The Cardiomyopathy Registry of the EURObservational Research Programme of the European Society of Cardiology: baseline data and contemporary management of adult patients with cardiomyopathies
Authors' conclusion
By providing contemporary observational data on characteristics and management of patients with cardiomyopathies, the registry provides a platform for the evaluation of guideline implementation.
Study context
- Population
- Adults with cardiomyopathy (hypertrophic cardiomyopathy (HCM), dilated cardiomyopathy (DCM), arrhythmogenic right ventricular cardiomyopathy (ARVC) or restrictive cardiomyopathy (RCM)) in the ESC EURObservational Cardiomyopathy Registry
- Participants
- 3,208 adults69 centres18 countries
- Exposure
- HCM vs DCM vs ARVC vs RCM
- HCMn = 1,739
- DCMn = 1,260
- ARVCn = 143
- RCMn = 66
- Outcome
- Baseline characteristics and management
Methodological detailsmultinational, consecutive patients, 69 centres in 18 countries
- Multinational
- Consecutive patients
- 69 centres in 18 countries
Main finding
As reported in the abstract
- Differences between cardiomyopathy subtypes in age at diagnosis, familial disease history, sustained ventricular arrhythmia history, MRI or genetic testing use, and defibrillator implantation
- P < 0.001
- Relatives vs probands: lower age at diagnosis
- P < 0.001
Observational data: associations, not effects.
Further findings
Pilot phase (more expert centres) vs Long-Term phase
- More frequent familial disease in Pilot phase
- P < 0.001
- More frequent diagnosis of rare underlying disease in Pilot phase
- P < 0.001
- More frequent defibrillator implantation in Pilot phase
- P = 0.023
Southern Europe vs other geographical areas (4 areas)
- More frequent familial disease in Southern Europe
- P < 0.001
- More frequent diagnosis via family screening in Southern Europe
- P < 0.001
- More frequent diagnosis of rare underlying disease in Southern Europe
- P < 0.001
Original publication
The Cardiomyopathy Registry of the EURObservational Research Programme of the European Society of Cardiology: baseline data and contemporary management of adult patients with cardiomyopathies. Eur Heart J. Published 24 January 2018. doi:10.
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